FITC标记的21号染色体开放阅读框13抗体
产品名称： FITC标记的21号染色体开放阅读框13抗体
英文名称： Anti-C21ORF13/FITC
产品编号： HZ-15123R-FITC
产品价格： null
产品产地： 中国/上海
品牌商标： HZbscience
更新时间： 2023-08-17T10:24:20
使用范围： ICC=1:50-200 IF=1:50-200
上海沪震实业有限公司
- 联系人 : 鲍丽雯
- 地址 : 上海市闵行区闵北路88弄1-30号第22幢AQ136室
- 邮编 : 200612
- 所在区域 : 上海
- 电话 : 139****0749
- 传真 : 021-60345367
- 邮箱 : www.shzbio.net
Rabbit Anti-C21ORF13/FITC Conjugated antibody
FITC标记的21号染色体开放阅读框13抗体
| 英文名称 | Anti-C21ORF13/FITC |
| 中文名称 | FITC标记的21号染色体开放阅读框13抗体 |
| 别 名 | C21orf13; Chromosome 21 open reading frame 13; Lca5l; LCA5L_HUMAN; Leber congenital amaurosis 5 like; Leber congenital amaurosis 5 like protein; Leber congenital amaurosis 5-like protein; Lebercilin-like protein; MGC33295; OTTHUMP00000069084; OTTHUMP00000069085. |
| 规格价格 | 100ul/2980元 购买 大包装/询价 |
| 说 明 书 | 100ul |
| 研究领域 | 细胞生物 免疫学 |
| 抗体来源 | Rabbit |
| 克隆类型 | Polyclonal |
| 交叉反应 | Human, Mouse, Rat, Horse, |
| 产品应用 | ICC=1:50-200 IF=1:50-200 not yet tested in other applications. optimal dilutions/concentrations should be determined by the end user. |
| 分 子 量 | 77kDa |
| 性 状 | Lyophilized or Liquid |
| 浓 度 | 1mg/ml |
| 免 疫 原 | KLH conjugated synthetic peptide derived from human C21ORF13 |
| 亚 型 | IgG |
| 纯化方法 | affinity purified by Protein A |
| 储 存 液 | 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol. |
| 保存条件 | Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C. |
| 产品介绍 | background: Leber congenital amaurosis (LCA) is one of the most common causes of hereditary blindness or severe visual impairment in infants. Mutations in several genes with diverse functions mapping to two loci have been implicated in LCA causation. These proteins are involved in processes such as photoreceptor development and maintenance, phototransduction, vitamin A metabolism and protein trafficking. LCA5, also known as Lebercilin, is a ciliary protein that is widely expressed during development and localizes to the connecting cilia of photoreceptors and to the microtubules, centrioles and primary cilia of cultured mammalian cells. The Leber congenital amaurosis 5-like protein (LCA5L) is a 670 amino acid protein that belongs to the LCA5 family. Similarity: Belongs to the LCA5 family. Database links: Entrez Gene: 150082 Human Entrez Gene: 385668 Mouse SwissProt: O95447 Human SwissProt: Q8C0X0 Mouse Unigene: 517284 Human Unigene: 24626 Mouse Important Note: This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications |
莱伯先天性黑蒙（LCA）是遗传性失明或婴幼儿严重视力损害最常见的原因之一。在LCA因果关系中，涉及到两个位点的不同功能的几个基因的突变被牵连。这些蛋白参与光受体的发育和维持、光转导、维生素A代谢和蛋白质运输等过程。LCA5又称Lebercilin，是一种在发育过程中广泛表达的睫状蛋白，定位于光感受器的连接纤毛以及培养的哺乳动物细胞的微管、中心粒和原生纤毛。莱伯先天性黑朦样蛋白（LCA5L）是属于LCA5家族的670个氨基酸。