FAH抗体-抗体-抗体-生物在线
FAH抗体

FAH抗体

商家询价

产品名称: FAH抗体

英文名称: FAHAntibody

产品编号: XY14928-1

产品价格: null

产品产地: 中国/美国

品牌商标: XYbscience

更新时间: 2023-08-17T09:55:27

使用范围: WB,ELISA,IHC-P,IHC-F,IF

上海信裕生物科技有限公司
  • 联系人 : 徐经理
  • 地址 : 上海市闵行莘庄工业区春东路508号A1-2F
  • 邮编 : 200612
  • 所在区域 : 上海
  • 电话 : 152****8802
  • 传真 : 021-37680378
  • 邮箱 : shxysw02@163.com

 FAH抗体

Applications
In-house applications ELISA, WB     Application not tested? Please see our Guarantee.
Published applications WB Publications 3 citations –view here
Species specificity Human,Mouse,Rat; other species not tested.
Published Species Human
Images
Prev1NextView more validation data
  • 14928-1-AP;mouse liver tissuemouse liver tissue were subjected to SDS PAGE followed by western blot with 14928-1-AP(FAH antibody) at dilution of 1:500
Positive WB detected in Mouse liver tissue, human liver tissue, rat liver tissue
Recommended dilution WB : 1:200-1:2000
 FAH抗体Application key: WB = Western blotting, IHC = Immunohistochemistry, IF = Immunofluorescence,
IP = Immunoprecipitation
Product Information
Source Rabbit Purification method Antigen affinity purification
Isotype IgG Storage PBS with 0.02% sodium azide and 50% glycerol pH 7.3. Store at -20oC.
Immunogen Information
Immunogen FAH fusion protein ag6704 Full name Fumarylacetoacetate hydrolase (fumarylacetoacetase)
Calculated molecular
weight
46 kDa Observed molecular 
weight
40-45kd
GenBank accession 
number
BC002527 Gene ID (NCBI) 2184
Gene symbol FAH Synonyms Beta diketonase, FAA, FAH, Fumarylacetoacetase, Fumarylacetoacetate hydrolase
Background FAH抗体

FAH is also named as FAA(fumarylacetoacetase), the last enzyme in tyrosine degradation, functionally important in the liver and kidney(PMID:8473520). FAH is a metabolic enzyme catalyzing the last step of tyrosine and phenylalanine catabolism: the hydrolysis of fumarylacetoacetate into acetoacetate and fumarate. In humans, deficiency of this activity is associated with the metabolic disease hereditary tyrosinaemia type I, which is also known as hepatorenal tyrosinaemia(PMID:17768357). FAH抗体

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