Moscerdam-表达分析-试剂-生物在线
Moscerdam

Moscerdam

商家询价

产品名称: Moscerdam

英文名称: Moscerdam

产品编号: Moscerdam

产品价格: 0

产品产地: Moscerdam

品牌商标: Moscerdam

更新时间: 2023-08-17T09:55:27

使用范围: null

上海信裕生物科技有限公司
  • 联系人 : 徐经理
  • 地址 : 上海市闵行莘庄工业区春东路508号A1-2F
  • 邮编 : 200612
  • 所在区域 : 上海
  • 电话 : 152****8802
  • 传真 : 021-37680378
  • 邮箱 : shxysw02@163.com

 

Moscerdam

Order Code Disease Substrate
INCL
   »»»»»»»»»
INCL; CLN1
newly available
4MU-6-thiopalmitoyl-beta-D-glucoside
    now available from Carbosynth (click INCL)
KRB Krabbe 6HMU-beta-D-galactoside
M2
   »»»»»»»»»
MPS II
discontinued
4MU-alpha-L-iduronide-2-sulphate
   no longer available, click M2 for alternative 
M3A
 
  »»»»»»»»»
MPS III A
newly available 
4MU-alpha-N-sulpho-D-glucosaminide
   now available from Carbosynth (click M3A)
M3C MPS III C 4MU-beta-D-glucosaminide
M3D
   »»»»»»»»»
MPS III D 
discontinued
4MU-alpha-N-acetyl-D-glucosaminide-6-sulphate
       no longer available, click M3D for alternative
M4A
   »»»»»»»»»
MPS IV A
discontinued
4MU-beta-D-galactoside-6-sulphate
       no longer available, click M4A for alternative
NPAB Niemann-Pick A/B 6HMU-phosphorylcholine
ANAGA Schindler 4MU-alpha-N-acetyl-D-galactosaminide


 

HMU 6-HMU-standard 6-hexadecanoylamino-4-methylumbelliferone

 

 

 

Fluorogenic substrates for the laboratory diagnosis of lysosomal storage diseases

 

  • Each lot is biochemically tested with fibroblasts from patients, 
    in an academic, lysosomal laboratory
  • Enzymes for "two-step" assays are included
  • Laboratory protocols are continuously upgraded through customer feedback